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Issue DateTitleAuthor(s)
7-May-2015A novel quantitative hemolytic assay coupled with restriction fragment length polymorphisms analysis enabled early diagnosis of atypical hemolytic uremic syndrome and identified unique predisposing mutations in Japan.Yoshida, Yoko; Miyata, Toshiyuki; Matsumoto, Masanori; Shirotani-Ikejima, Hiroko; Uchida, Yumiko; Ohyama, Yoshifumi; Kokubo, Tetsuro; Fujimura, Yoshihiro
May-2012ADAMTS13 activity may predict the cumulative survival of patients with liver cirrhosis in comparison with the Child-Turcotte-Pugh score and the Model for End-Stage Liver Disease score.Takaya, Hiroaki; Uemura, Masahito; Fujimura, Yoshihiro; Matsumoto, Masanori; Matsuyama, Tomomi; Kato, Seiji; Morioka, Chie; Ishizashi, Hiromichi; Hori, Yuji; Fujimoto, Masao; Tsujimoto, Tatsuhiro; Kawaratani, Hideto; Toyohara, Masahisa; Kurumatani, Norio; Fukui, Hiroshi
Dec-2013ADAMTS13 unbound to larger von Willebrand factor multimers in cryosupernatant: Implications for selection of plasma preparations for TTP treatmentHori, Yuji; Hayakawa, Masaki; Isonishi, Ayami; Soejima, Kenji; Matsumoto, Masanori; Fujimura, Yoshihiro
28-Feb-2006ADAMTS13解析によるTTP/HUS診断松本, 雅則; 石指, 宏通; 八木, 秀男; 藤村, 吉博
Nov-2022Age and composition of the thrombus retrieved by mechanical thrombectomy from patients with acute ischemic stroke are associated with revascularization and clinical outcomes.Shimizu, Hisao; Hatakeyama, Kinta; Saito, Kozue; Shobatake, Ryogo; Takahashi, Nobuyuki; Deguchi, Jun; Tokunaga, Hidemori; Shimada, Keiji; Nakagawa, Ichiro; Myochin, Kaoru; Sakai, Kazuya; Kubo, Masayuki; Yamashita, Atsushi; Obayashi, Chiho; Sugie, Kazuma; Matsumoto, Masanori
7-Oct-2021Analysis focusing on plasma von Willebrand factor in pachychoroid neovasculopathy and age-related macular degeneration.Hirai, Hiromasa; Yamashita, Mariko; Matsumoto, Masanori; Hayakawa, Masaki; Sakai, Kazuya; Ueda, Tetsuo; Ogata, Nahoko
Jun-2019Blood group antigen A on von Willebrand factor is more protective against ADAMTS13 cleavage than antigens B and H.Hayakawa, Masaki; Kato, Seiji; Matsui, Taei; Sakai, Kazuya; Fujimura, Yoshihiro; Matsumoto, Masanori
Oct-2018Complement activation associated with ADAMTS13 deficiency may contribute to the characteristic glomerular manifestations in Upshaw-Schulman syndrome.Itami, Hiroe; Hara, Shigeo; Matsumoto, Masanori; Imamura, Shin; Kanai, Rie; Nishiyama, Kei; Ishimura, Masataka; Ohga, Shouichi; Yoshida, Makiko; Tanaka, Ryojiro; Ogawa, Yoshiyuki; Asada, Yujiro; Sekita-Hatakeyama, Yoko; Hatakeyama, Kinta; Ohbayashi, Chiho
Aug-2017Implementation of a rapid assay of ADAMTS13 activity was associated with improved 30-day survival rate in patients with acquired primary thrombotic thrombocytopenic purpura who received platelet transfusions.Yoshii, Yumi; Fujimura, Yoshihiro; Bennett, Charles L.; Isonishi, Ayami; Kurumatani, Norio; Matsumoto, Masanori
24-Jan-2018Intravitreal injection of aflibercept, an anti-VEGF antagonist, down-regulates plasma von Willebrand factor in patients with age-related macular degeneration.Yamashita, Mariko; Matsumoto, Masanori; Hayakawa, Masaki; Sakai, Kazuya; Fujimura, Yoshihiro; Ogata, Nahoko
Jul-2019Involvement of the ADAMTS13-VWF axis in acute Kawasaki disease and effects of intravenous immunoglobulin.Tsujii, Nobuyuki; Nogami, Keiji; Matsumoto, Masanori; Yoshizawa, Hiroyuki; Takase, Toshio; Tanaka, Ichiro; Sakai, Toshiyuki; Fukuda, Kazuyoshi; Hayakawa, Masaki; Sakai, Kazuya; Isonishi, Ayami; Matsuura, Kayoko; Fujimura, Yoshihiro; Shima, Midori
Nov-2019Ischaemia-reperfusion injury with Pringle's maneuver induces unusually large von Willebrand factor multimers after hepatectomy.Yoshikawa, Takahiro; Nomi, Takeo; Sakai, Kazuya; Hayakawa, Masaki; Hokuto, Daisuke; Matsuo, Yasuko; Sho, Masayuki; Matsumoto, Masanori
22-Jul-2011Natural history of Upshaw-Schulman syndrome based on ADAMTS13 gene analysis in JapanFujimura, Yoshihiro; Matsumoto, Masanori; Isonishi, Ayami; Yagi, Hideo; Kokame, Koichi; Soejima, Kenji; Murata, Mitsuru; Miyata, Toshiyuki
19-Dec-2019Novel aptamer to von Willebrand factor A1 domain (TAGX-0004) shows total inhibition of thrombus formation superior to ARC1779 and comparable to caplacizumab.Sakai, Kazuya; Someya, Tatsuhiko; Harada, Kaori; Yagi, Hideo; Matsui, Taei; Matsumoto, Masanori
1-Jan-2020Plasma Level of von Willebrand Factor Propeptide at Diagnosis: A Marker of Subsequent Renal Dysfunction in Autoimmune Rheumatic Diseases.Yada, Noritaka; Yoshimoto, Kiyomi; Kawashima, Hiromasa; Yoneima, Ryo; Nishimura, Nobushiro; Tai, Yoshiaki; Tsushima, Emiko; Miyamoto, Makiko; Ono, Shiro; Matsumoto, Masanori; Fujimoto, Takashi; Nishio, Kenji
Oct-2015Poor responder to plasma exchange therapy in acquired thrombotic thrombocytopenic purpura is associated with ADAMTS13 inhibitor boosting: visualization of an ADAMTS13 inhibitor complex and its proteolytic clearance from plasma.Isonishi, Ayami; Bennett, Charles L.; Plaimauer, Barbara; Scheiflinger, Friedrich; Matsumoto, Masanori; Fujimura, Yoshihiro
1-Oct-2016Rapid Restoration of Thrombus Formation and High-Molecular-Weight von Willebrand Factor Multimers in Patients with Severe Aortic Stenosis After Valve Replacement.Yamashita, Keigo; Yagi, Hideo; Hayakawa, Masaki; Abe, Takehisa; Hayata, Yoshihiro; Yamaguchi, Naoko; Sugimoto, Mitsuhiko; Fujimura, Yoshihiro; Matsumoto, Masanori; Taniguchi, Shigeki
May-2013Ratio of von Willebrand factor propeptide to ADAMTS13 is associated with severity of sepsis.Fukushima, Hidetada; Nishio, Kenji; Asai, Hideki; Watanabe, Tomoo; Seki, Tadahiko; Matsui, Hideto; Sugimoto, Mitsuhiko; Matsumoto, Masanori; Fujimura, Yoshihiro; Okuchi, Kazuo
Sep-2012Reduced larger von Willebrand factor multimers at dawn in OSA plasmas reflect severity of apnoeic episodes.Koyama, Noriko; Matsumoto, Masanori; Tamaki, Shinji; Yoshikawa, Masanori; Fujimura, Yoshihiro; Kimura, Hiroshi
Oct-2021Strong association between insufficient plasma exchange and fatal outcomes in Japanese patients with immune-mediated thrombotic thrombocytopenic purpura.Kayashima, Michinori; Sakai, Kazuya; Harada, Kazuki; Kanetake, Jun; Kubo, Masayuki; Hamada, Eriko; Hayakawa, Masaki; Hatakeyama, Kinta; Matsumoto, Masanori
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